ROP-ET: a prospective phase III trial investigating the efficacy and safety of ropeginterferon alfa-2b in essential thrombocythemia patients with limited treatment options


Por: Kiladjian, JJ, Marin, FF, Al-Ali, HK, Alvarez-Larrán, A, Beggiato, E, Bieniaszewska, M, Breccia, M, Buxhofer-Ausch, V, Cerna, O, Crisan, AM, Danaila, CD, De Stefano, V, Döhner, K, Empson, V, Gora-Tybor, J, Griesshammer, M, Grosicki, S, Guglielmelli, P, García-Gutierrez, V, Heidel, FH, Illés, A, Tomuleasa, C, James, C, Koschmieder, S, Krauth, MT, Krejcy, K, Lazaroiu, MC, Mayer, J, Nagy, ZG, Nicolini, FE, Palandri, F, Pappa, V, Reiter, AJ, Sacha, T, Schlager, S, Schmidt, S, Terpos, E, Unger, M, Wölfler, A, Cirici, BX and Klade, C

Publicada: 1 jul 2024 Ahead of Print: 1 mar 2024
Resumen:
Interferon-based therapies, such as ropeginterferon alfa-2b have emerged as promising disease-modifying agents for myeloproliferative neoplasms (MPNs), including essential thrombocythemia (ET). Current ET treatments aim to normalize hematological parameters and reduce the thrombotic risk, but they do not modify the natural history of the disease and hence, have no impact on disease progression. Ropeginterferon alfa-2b (trade name BESREMi (R)), a novel, monopegylated interferon alfa-2b with an extended administration interval, has demonstrated a robust and sustained efficacy in polycythemia vera (PV) patients. Given the similarities in disease pathophysiology and treatment goals, ropeginterferon alfa-2b holds promise as a treatment option for ET. The ROP-ET trial is a prospective, multicenter, single-arm phase III study that includes patients with ET who are intolerant or resistant to, and/or are ineligible for current therapies, such as hydroxyurea (HU), anagrelide (ANA), busulfan (BUS) and pipobroman, leaving these patients with limited treatment options. The primary endpoint is a composite response of hematologic parameters and disease-related symptoms, according to modified European LeukemiaNet (ELN) criteria. Secondary endpoints include improvements in symptoms and quality of life, molecular response and the safety profile of ropeginterferon alfa-2b. Over a 3-year period the trial assesses longer term outcomes, particularly the effects on allele burden and clinical outcomes, such as disease-related symptoms, vascular events and disease progression. No prospective clinical trial data exist for ropeginterferon alfa-2b in the planned ET study population and this study will provide new findings that may contribute to advancing the treatment landscape for ET patients with limited alternatives.

Filiaciones:
Kiladjian, JJ:
 Univ Paris Cite, CIC 1427, Inserm, F-75010 Paris, France

 Hop St Louis, AP HP, Ctr Invest Clin, F-75010 Paris, France

Marin, FF:
 UCAM IMIB Murcia, Morales Meseguer Univ Gen Hosp, Reg Ctr Blood Donat, CIBERER, Murcia, Spain

Al-Ali, HK:
 Univ Hosp Halle Saale, Krukenberg Canc Ctr Halle, Halle, Germany

Alvarez-Larrán, A:
 Hosp Clin Barcelona, Dept Hematol, Barcelona, Spain

Beggiato, E:
 Univ Hosp City Hlth & Sci Turin, Hosp Molinette, Complex Struct Hematol, Turin, Italy

Bieniaszewska, M:
 Med Univ Gdansk, Gdansk, Poland

Breccia, M:
 Sapienza Univ Rome, Dept Translat & Precis Med, Rome, Italy

Buxhofer-Ausch, V:
 Johannes Kepler Univ Linz, Dept Internal Med Hematol Stem Cell Transplantat, Ordensklinikum Linz Elisabethinen, Linz, Austria

 Johannes Kepler Univ Linz, Med Fac, Linz, Austria

Cerna, O:
 Univ Hosp Kralovske Vinohrady, Clin Internal Hematol, Prague, Czech Republic

Crisan, AM:
 Fundeni Clin Inst, Ctr Hematol & Bone Marrow Transplantat, Bucharest, Romania

Danaila, CD:
 Reg Inst Oncol, Dept Clin Hematol, Iasi, Romania

De Stefano, V:
 Catholic Univ, Fdn Policlin Gemelli IRCCS, Sect Hematol, Rome, Italy

Döhner, K:
 Univ Hosp Ulm, Dept Internal Med 3, Ulm, Germany

Empson, V:
 AOP Hlth, Vienna, Austria

Gora-Tybor, J:
 Copernicus Mem Hosp, Dept Hematooncol, Lodz, Poland

 Med Univ Lodz, Dept Hematol, Lodz, Poland

Griesshammer, M:
 Ruhr Univ Bochum, Johannes Wesling Hosp Minden, Dept Oncol & Hematol, Minden, Germany

Grosicki, S:
 Med Univ Silesia, Katowice, Poland

Guglielmelli, P:
 Careggi Univ Hosp, Dept Hematol, Florence, Italy

García-Gutierrez, V:
 Hosp Univ Ramon y Cajal IRYCIS, Madrid, Spain

 Univ Alcala, Madrid, Spain

Heidel, FH:
 Hannover Med Sch MHH, Clin Hematol Hemostasis Oncol & Stem Cell Transpl, Hannover, Germany

Illés, A:
 Univ Debrecen, Fac Med, Dept Internal Med, Div Hematol, Debrecen, Hungary

Tomuleasa, C:
 Iuliu Hatieganu Univ Med & Pharm, Ion Chiricuta Inst Oncol, Hematol Dept, Cluj Napoca, Romania

 Iuliu Hatieganu Univ Med & Pharm, Medfuture Res Ctr Adv Med, Cluj Napoca, Romania

James, C:
 Univ Bordeaux, INSERM, BMC, U1034, F-33600 Pessac, France

 Bordeaux Univ Hosp, Lab Hematol, Bordeaux, France

Koschmieder, S:
 Rhein Westfal TH Aachen, Fac Med, Dept Hematol Oncik Genistasteol & Stem cell Trans, Med Clin 4, Aachen, Germany

Krauth, MT:
 Med Univ Vienna, Dept Internal Med 1, Clin Dept Hematol & Hemostaseol, Vienna, Austria

Krejcy, K:
 AOP Hlth, Vienna, Austria

Lazaroiu, MC:
 Policlin Diagnost Rapid Brasov, Dept Hematol, Brasov, Romania

Mayer, J:
 Univ Hosp Brno, Masaryk Univ, Dept Internal Med Hematol & Oncol, Brno, Czech Republic

Nagy, ZG:
 Semmelweis Univ, Dept Internal Med & Hematol, Div Hematol, Budapest, Hungary

Nicolini, FE:
 Ctr Leon Berard, Lyon, France

Palandri, F:
 IRCCS Azienda Osped Univ Bologna, Bologna, Italy

 Ist Ematol Seragnoli, Bologna, Italy

Pappa, V:
 Univ Gen Hosp Attikon, Athens, Greece

Reiter, AJ:
 Univ Hosp Mannheim, Med Clin Hematol & Internist Oncol 3, Mannheim, Germany

Sacha, T:
 Jagiellonian Univ Hosp, Dept Hematol, Krakow, Poland

Schlager, S:
 AOP Hlth, Vienna, Austria

Schmidt, S:
 Med Univ Innsbruck, Dept Internal Med Hematol & Oncol 5, Innsbruck, Austria

Terpos, E:
 Natl & Kapodistrian Univ Athens, Sch Med, Dept Clin Therapeut, Athens, Greece

Unger, M:
 AOP Hlth, Vienna, Austria

Wölfler, A:
 Med Univ Graz, Dept Internal Med, Clin Div Hematol, Graz, Austria

:
 Univ Autonoma Barcelona, Hosp Germans Trias i Pujol, Josep Carreras Leukemia Res Inst, Inst Catala Oncol, Barcelona, Spain

Klade, C:
 AOP Hlth, Vienna, Austria
ISSN: 09395555





Annals of Hematology
Editorial
Springer Verlag, ONE NEW YORK PLAZA, SUITE 4600, NEW YORK, NY, UNITED STATES, Alemania
Tipo de documento: Article
Volumen: 103 Número: 7
Páginas: 2299-2310
WOS Id: 001182326400002
ID de PubMed: 38438627
imagen Green Published, hybrid

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