Impaired condensin complex and Aurora B kinase underlie mitotic and chromosomal defects in hyperdiploid B-cell ALL


Por: Molina, O, Vinyoles, M, Granada, I, Roca-Ho, H, Gutierrez-Aguera, F, Valledor, L, Lopez-Lopez, CM, Rodriguez-Gonzalez, P, Trincado, JL, Menendez, SPIT, Pal, D, Ballerini, P, den Boer, ML, Plensa, I, Perez-Iribarne, MM, Rodriguez-Perales, S, Calasanz, MJ, Ramirez-Orellana, M, Rodriguez, R, Camos, M, Calvo, M, Bueno, C and Menendez, P

Publicada: 16 jul 2020
Resumen:
B-cell acute lymphoblastic leukemia (ALL; B-ALL) is the most common pediatric cancer, and high hyperdiploidy (HyperD) identifies the most common subtype of pediatric B-ALL. Despite HyperD being an initiating oncogenic event affiliated with childhood B-ALL, the mitotic and chromosomal defects associated with HyperD B-ALL (HyperD-ALL) remain poorly characterized. Here, we have used 54 primary pediatric B-ALL samples to characterize the cellular-molecular mechanisms underlying the mitotic/chromosome defects predicated to be early pathogenic contributors in HyperD-ALL. We report that HyperD-ALL blasts are low proliferative and show a delay in early mitosis at prometaphase, associated with chromosome-alignment defects at the metaphase plate leading to robust chromosome-segregation defects and nonmodal karyotypes. Mechanistically, biochemical, functional, and mass-spectrometry assays revealed that condensin complex is impaired in HyperD-ALL cells, leading to chromosome hypocondensation, loss of centromere stiffness, and mislocalization of the chromosome passenger complex proteins Aurora B kinase (AURKB) and Survivin in early mitosis. HyperD-ALL cells show chromatid cohesion defects and an impaired spindle assembly checkpoint (SAC), thus undergoing mitotic slippage due to defective AURKB and impaired SAC activity, downstream of condensin complex defects. Chromosome structure/condensation defects and hyperdiploidy were reproduced in healthy CD34(+) stem/progenitor cells upon inhibition of AURKB and/or SAC. Collectively, hyperdiploid B-ALL is associated with a defective condensin complex, AURKB, and SAC.

Filiaciones:
:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

:
 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

 Germans Trias & Pujol Univ Hosp, Hematol Lab, Catalan Inst Oncol, Badalona, Spain

Roca-Ho, H:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

Valledor, L:
 Univ Oviedo, Dept Phys & Analyt Chem, Asturias, Spain

Lopez-Lopez, CM:
 Univ Oviedo, Dept Phys & Analyt Chem, Asturias, Spain

Rodriguez-Gonzalez, P:
 Univ Oviedo, Dept Phys & Analyt Chem, Asturias, Spain

:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

Menendez, SPIT:
 Hosp Univ Cent Asturias, Inst Invest Sanitaria Principado Asturias ISPA, Oviedo, Spain

 ISCIII, CIBER ONC, Madrid, Spain

Pal, D:
 Newcastle Univ, Northern Inst Canc Res, Wolfson Childhood Canc Res Ctr, Newcastle Upon Tyne, Tyne & Wear, England

 Northumbria Univ, Dept Appl Sci, Newcastle Upon Tyne, Tyne & Wear, England

Ballerini, P:
 A Trousseau Hosp, Pediat Hematol, Paris, France

den Boer, ML:
 Princess Maxima Ctr Pediat Oncol, Utrecht, Netherlands

Plensa, I:
 Inst Recerca Hosp St Joan de Deu, Hematol Lab, Barcelona, Spain

Perez-Iribarne, MM:
 Inst Recerca Hosp St Joan de Deu, Hematol Lab, Barcelona, Spain

Rodriguez-Perales, S:
 Ctr Nacl Invest Oncol, Mol Cytogenet Grp, Madrid, Spain

Calasanz, MJ:
 Univ Navarra, CIMA Lab Diagnost, Pamplona, Spain

Ramirez-Orellana, M:
 Hosp Nino Jesus, Hematol Diagnost Lab, Madrid, Spain

Rodriguez, R:
 Hosp Univ Cent Asturias, Inst Invest Sanitaria Principado Asturias ISPA, Oviedo, Spain

 ISCIII, CIBER ONC, Madrid, Spain

Camos, M:
 Inst Recerca Hosp St Joan de Deu, Hematol Lab, Barcelona, Spain

 Inst Recerca Hosp St Joan de Deu, Dev Tumors Biol Grp, Leukemia & Other Pediat Hemopathies, Barcelona, Spain

 ISCIII, Ctr Invest Biomed Red Enfermedades Raras CIBERER, Barcelona, Spain

Calvo, M:
 Univ Barcelona CCiTUB, Sci Ctr, Campus Clin, Barcelona, Spain

 Univ Barcelona CCiTUB, Technol Ctr, Campus Clin, Barcelona, Spain

:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

:
 Josep Carreras Leukemia Res Inst, Barcelona, Spain

 Univ Barcelona, Sch Med, Dept Biomed, Barcelona, Spain

 Inst Salud Carlos III ISCIII, Ctr Invest Biomed Red Canc CIBER ONC, Barcelona, Spain

 Inst Catalana Recerca & Estudis Avancats ICREA, Barcelona, Spain
ISSN: 00064971





Blood
Editorial
American Society of Hematology, 2021 L ST NW, SUITE 900, WASHINGTON, DC 20036 USA, Estados Unidos America
Tipo de documento: Article
Volumen: 136 Número: 3
Páginas: 313-327
WOS Id: 000550485600010
ID de PubMed: 32321174
imagen Green Accepted, Green Published, Bronze

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