Long-term disability trajectories in primary progressive MS patients: A latent class growth analysis


Por: Signori, A, Izquierdo, G, Lugaresi, A, Hupperts, R, Grand'Maison, F, Sola, P, Horakova, D, Havrdova, E, Prat, A, Girard, M, Duquette, P, Boz, C, Grammond, P, Terzi, M, Singhal, B, Alroughani, R, Petersen, T, Ramo, C, Oreja-Guevara, C, Spitaleri, D, Shaygannejad, V, Butzkueven, H, Kalincik, T, Jokubaitis, V, Slee, M, Bolanos, RF, Sanchez-Menoyo, JL, Pucci, E, Granella, F, Lechner-Scott, J, Iuliano, G, Hughes, S, Bergamaschi, R, Taylor, B, Verheul, F, Rio, ME, Amato, MP, Sajedi, SA, Majdinasab, N, Van Pesch, V, Sormani, MP and Trojano, M

Publicada: 1 abr 2018
Resumen:
Background: Several natural history studies on primary progressive multiple sclerosis (PPMS) patients detected a consistent heterogeneity in the rate of disability accumulation. Objectives: To identify subgroups of PPMS patients with similar longitudinal trajectories of Expanded Disability Status Scale (EDSS) over time. Methods: All PPMS patients collected within the MSBase registry, who had their first EDSS assessment within 5 years from onset, were included in the analysis. Longitudinal EDSS scores were modeled by a latent class mixed model (LCMM), using a nonlinear function of time from onset. LCMM is an advanced statistical approach that models heterogeneity between patients by classifying them into unobserved groups showing similar characteristics. Results: A total of 853 PPMS (51.7% females) from 24 countries with a mean age at onset of 42.4 years (standard deviation (SD): 10.8 years), a median baseline EDSS of 4 (interquartile range (IQR): 2.5-5.5), and 2.4 years of disease duration (SD: 1.5 years) were included. LCMM detected three different subgroups of patients with a mild (n = 143; 16.8%), moderate (n = 378; 44.3%), or severe (n = 332; 38.9%) disability trajectory. The probability of reaching EDSS 6 at 10 years was 0%, 46.4%, and 81.9% respectively. Conclusion: Applying an LCMM modeling approach to long-term EDSS data, it is possible to identify groups of PPMS patients with different prognosis.

Filiaciones:
Signori, A:
 Univ Genoa, Sect Biostat, Dept Hlth Sci DISSAL, Via A Pastore 1, I-16132 Genoa, Italy

Izquierdo, G:
 Hosp Univ Virgen Macarena, Seville, Spain

Lugaresi, A:
 Univ Bologna, Dept Biomed & Neuromotor Sci DIBINEM, Alma Mater Studiorum, Bologna, Italy

 IRCCS Ist Sci Neurol Bologna, Bologna, Italy

Hupperts, R:
 Zuyderland Ziekenhuis, Sittard, Netherlands

Grand'Maison, F:
 Clin Neuro Rive Sud, Greenfield Pk, PQ, Canada

Sola, P:
 Nuovo Osped Civile S Agostino Estense, Modena, Italy

Horakova, D:
 Charles Univ Prague, Fac Med 1, Dept Neurol, Prague, Czech Republic

 Charles Univ Prague, Fac Med 1, Ctr Clin Neurosci, Prague, Czech Republic

 Gen Univ Hosp Prague, Prague, Czech Republic

Havrdova, E:
 Charles Univ Prague, Fac Med 1, Dept Neurol, Prague, Czech Republic

 Charles Univ Prague, Fac Med 1, Ctr Clin Neurosci, Prague, Czech Republic

 Gen Univ Hosp Prague, Prague, Czech Republic

Prat, A:
 Hop Notre Dame De Bon Secours, Montreal, PQ, Canada

Girard, M:
 Hop Notre Dame De Bon Secours, Montreal, PQ, Canada

Duquette, P:
 Hop Notre Dame De Bon Secours, Montreal, PQ, Canada

Boz, C:
 Farabi Hosp, KTU Med Fac, Trabzon, Turkey

Grammond, P:
 Ctr Readaptat Deficience Phys Chaudiere Appalache, Levis, PQ, Canada

Terzi, M:
 Ondokuz Mayis Univ, Fac Med, Samsun, Turkey

Singhal, B:
 BHIMS, Bombay, Maharashtra, India

Alroughani, R:
 Amiri Hosp, Kuwait, Kuwait

Petersen, T:
 Kommunehospitalet, Aarhus, Denmark

:
 Hosp Badalona Germans Trias & Pujol, Badalona, Spain

Oreja-Guevara, C:
 Hosp Clin San Carlos, Madrid, Spain

Spitaleri, D:
 Azienda Osped Rilievo Nazl, Avellino, Italy

Shaygannejad, V:
 Isfahan Univ Med Sci, Esfahan, Iran

Butzkueven, H:
 Box Hill Hosp, Melbourne, Vic, Australia

 Univ Melbourne, Dept Med, Melbourne, Vic, Australia

Kalincik, T:
 Univ Melbourne, Dept Med, Melbourne, Vic, Australia

Jokubaitis, V:
 Univ Melbourne, Dept Med, Melbourne, Vic, Australia

Slee, M:
 Flinders Univ & Med Ctr, Adelaide, SA, Australia

Bolanos, RF:
 Hosp Univ Virgen de Valme, Seville, Spain

Sanchez-Menoyo, JL:
 Hosp Galdakao Usansolo, Galdakao, Spain

Pucci, E:
 Azienda Sanit Unica Reg Marche, UOC Neurol, Macerata, Italy

Granella, F:
 Univ Parma, Parma, Italy

Lechner-Scott, J:
 Univ Newcastle, Hunter Med Res Inst, Newcastle, NSW, Australia

Iuliano, G:
 Osped Riuniti Salerno, Salerno, Italy

Hughes, S:
 Craigavon Area Hosp, Craigavon, North Ireland

Bergamaschi, R:
 C Mondino Natl Neurol Inst, Pavia, Italy

Taylor, B:
 Royal Hobart Hosp, Hobart, Tas, Australia

Verheul, F:
 Groene Hart Ziekenhuis, Gouda, Netherlands

Rio, ME:
 Hosp Sao Joao, Porto, Portugal

Amato, MP:
 Univ Florence, Sect Neurosci, Dept NEUROFARBA, Florence, Italy

Sajedi, SA:
 Golestan Univ Med Sci, Dept Neurol, Gorgan, Iran

 Ahvaz Jundishapur Univ Med Sci, Golestan Hosp, Ahvaz, Iran

Majdinasab, N:
 Ahvaz Jundishapur Univ Med Sci, Golestan Hosp, Ahvaz, Iran

Van Pesch, V:
 Clin Univ St Luc, Brussels, Belgium

Sormani, MP:
 Univ Genoa, Sect Biostat, Dept Hlth Sci DISSAL, Via A Pastore 1, I-16132 Genoa, Italy

Trojano, M:
 Univ Bari, Dept Basic Med Sci Neurosci & Sense Organs, Bari, Italy
ISSN: 13524585





MULTIPLE SCLEROSIS JOURNAL
Editorial
SAGE Publications, 1 OLIVERS YARD, 55 CITY ROAD, LONDON EC1Y 1SP, ENGLAND, Estados Unidos America
Tipo de documento: Article
Volumen: 24 Número: 5
Páginas: 642-652
WOS Id: 000432098100013
ID de PubMed: 28382837

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