Autogenous Control of 5 ' TOP mRNA Stability by 40S Ribosomes


Por: Gentilella, A, Moron-Duran, FD, Fuentes, P, Zweig-Rocha, G, Riano-Canalias, F, Pelletier, J, Ruiz, M, Turon, G, Castano, J, Tauler, A, Bueno, C, Menendez, P, Kozma, SC and Thomas, G

Publicada: 6 jul 2017
Resumen:
Ribosomal protein (RP) expression in higher eukaryotes is regulated translationally through the 5'TOP sequence. This mechanism evolved to more rapidly produce RPs on demand in different tissues. Here we show that 40S ribosomes, in a complex with the mRNA binding protein LARP1, selectively stabilize 5'TOP mRNAs, with disruption of this complex leading to induction of the impaired ribosome biogenesis checkpoint (IRBC) and p53 stabilization. The importance of this mechanism is underscored in 5q(-) syndrome, a macrocytic anemia caused by a large monoallelic deletion, which we found to also encompass the LARP1 gene. Critically, depletion of LARP1 alone in human adult CD34+ bone marrow precursor cells leads to a reduction in 5'TOP mRNAs and the induction of p53. These studies identify a 40S ribosome function independent of those in translation that, with LARP1, mediates the autogenous control of 5'TOP mRNA stability, whose disruption is implicated in the pathophysiology of 5q(-) syndrome.

Filiaciones:
Gentilella, A:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

 Univ Barcelona, Fac Pharm, Dept Biochem & Physiol, E-08028 Barcelona, Spain

Moron-Duran, FD:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

Fuentes, P:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

 Univ Autonoma Barcelona, Dept Surg & Morphol Sci, Vail dHebron Inst Recerca, Barcelona 08035, Spain

Zweig-Rocha, G:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

Riano-Canalias, F:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

Pelletier, J:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

Ruiz, M:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

Turon, G:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

 Inst Res Biomed, Baldiri Reixac 10, Barcelona 08028, Spain

Castano, J:
 Univ Cincinnati, Sch Med, Dept Internal Med, Div Hematol Oncol, Cincinnati, OH 45267 USA

Tauler, A:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

 Univ Barcelona, Fac Pharm, Dept Biochem & Physiol, E-08028 Barcelona, Spain

:
 Univ Barcelona, Josep Carreras Leukemia Res Inst, Barcelona 08916, Spain

 Univ Barcelona, Sch Med, Barcelona 08916, Spain

:
 Univ Barcelona, Josep Carreras Leukemia Res Inst, Barcelona 08916, Spain

 Univ Barcelona, Sch Med, Barcelona 08916, Spain

 Inst Catala Recerca & Estudis Avangats ICREA Llui, Barcelona 08916, Spain

Kozma, SC:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

 Univ Cincinnati, Sch Med, Dept Internal Med, Div Hematol Oncol, Cincinnati, OH 45267 USA

Thomas, G:
 IDIBELL, Bellvitge Biomed Res Inst, Mol Mech & Expt Therapy Oncol Program, Metab & Canc Grp, Barcelona 08908, Spain

 Univ Cincinnati, Sch Med, Dept Internal Med, Div Hematol Oncol, Cincinnati, OH 45267 USA

 Univ Barcelona, Fac Med & Hlth Sci, Physiol Sci Dept, Barcelona 08908, Spain
ISSN: 10974164





Molecular Cell
Editorial
Cell Press, 50 HAMPSHIRE ST, FLOOR 5, CAMBRIDGE, MA 02139 USA, Estados Unidos America
Tipo de documento: Article
Volumen: 67 Número: 1
Páginas: 55
WOS Id: 000404897300007
ID de PubMed: 28673543
imagen Bronze, Green Accepted

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